NCI Definition: A choroid plexus papilloma characterized by increased mitotic activity. [1]

Atypical choroid plexus papillomas most frequently harbor alterations in TP53, IDH1, ZRSR2, ZFHX3, and TET2 [2].

Most Commonly Altered Genes in Atypical Choroid Plexus Papilloma

TP53 c.217-c.1178 Missense, TP53 Mutation, TP53 Missense, IDH1 Mutation, and TP53 Exon 8 Mutation are the most common alterations in atypical choroid plexus papilloma [2].

Top Alterations in Atypical Choroid Plexus Papilloma

Disease Details

Choroid Plexus Neoplasm
OncoTree Name
Atypical Choroid Plexus Papilloma
OncoTree Code


1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 8. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.