Overview

NCI Definition: An aggressive malignant embryonal neoplasm arising from the central nervous system. This category includes ependymoblastoma, medulloepithelioma, and supratentorial primitive neuroectodermal tumor. It usually follows an aggressive clinical course. [1]

Disease Details

Synonyms
CNS Primitive Neuroectodermal Neoplasm, Central Nervous System Primitive Neuroectodermal Tumor (WHO Grade IV), CNS Primitive Neuroectodermal Tumor, CNS PNET, Central Primitive Neuroectodermal Neoplasm, Central Nervous System Primitive Neuroectodermal Neoplasm, Central Nervous System PNET, Central Primitive Neuroectodermal Tumor
Parent(s)
Malignant Infratentorial Neoplasm

References

1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 6. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.