NCI Definition: A sarcoma that arises from the central nervous system. [1]

Significant Genes in Central Nervous System Sarcoma

H3F3A +

Disease Details

Sarcoma of the Central Nervous System, Sarcoma of the CNS, Sarcoma of Central Nervous System, CNS Sarcoma, Sarcoma of CNS
Soft Tissue Sarcoma
Intracranial Liposarcoma, Central Nervous System Fibrosarcoma, Spinal Cord Sarcoma, Central Nervous System Mesenchymal Chondrosarcoma, Meningeal Sarcoma, Central Nervous System Rhabdomyosarcoma, Brain Sarcoma, and Central Nervous System Angiosarcoma


1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 8. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.