Overview

NCI Definition: A rare malignant soft tissue neoplasm of uncertain differentiation, characterized by the presence of chondroblast-like cells in a myxoid stroma and a multinodular growth pattern. The most common sites of involvement are the deep soft tissues of the extremities, particularly the thigh. It usually presents as an enlarging soft tissue mass. Patients may have long survivals, but local recurrences and metastases occur in approximately half of the cases. The most common site of metastasis is the lungs. [1]

Disease Details

Synonyms
Extraosseous Chondrosarcoma, Extraskeletal Chondrosarcoma, Myxoid Extraskeletal Chondrosarcoma, EMC, Myxoid Extraosseous Chondrosarcoma
Parent(s)
Myxoid Chondrosarcoma
Children
Intracranial Extraskeletal Myxoid Chondrosarcoma
OncoTree Name
Extraskeletal Myxoid Chondrosarcoma
OncoTree Code
EMCHS

References

1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 6. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.