NCI Definition: A well differentiated mucinous adenocarcinoma that arises from the appendix. It is characterized by slow growth and it is associated with the development of pseudomyxoma peritonei. Unlike the high grade mucinous adenocarcinoma of the appendix, it usually does not spread beyond the peritoneum and it does not metastasize to distant anatomic sites. [1]

Disease Details

LAMN, Appendix Well Differentiated Mucinous Adenocarcinoma, Low-Grade Appendix Mucinous Neoplasm
Appendix Mucinous Adenocarcinoma
OncoTree Name
Low-grade Appendiceal Mucinous Neoplasm
OncoTree Code


1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 8. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.