Overview

NCI Definition: A small round cell tumor with neural differentiation arising from the soft tissues or bone. [1]

Significant Genes in Peripheral Primitive Neuroectodermal Tumor

BRCA1 +

BRCA2 +

Disease Details

Synonyms
Peripheral Neuroepithelioma, Peripheral PNET, Peripheral Neuroectodermal Tumor, Peripheral Neuroectodermal Neoplasm, Peripheral Primitive Neuroectodermal Neoplasm, pPNET
Parent(s)
Primitive Neuroectodermal Tumor
Children
Peripheral Primitive Neuroectodermal Tumor of Soft Tissues and Peripheral Primitive Neuroectodermal Tumor of Bone

References

1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 6. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.