Overview

NCI Definition: A localized neoplasm of probable fibroblastic derivation. It is characterized by the presence of round to spindle-shaped cells, hylanized stroma formation, thin-walled branching blood vessels, and thin bands of collagen. [1]

Disease Details

Synonyms
Localized Fibrous Tumor, Submesothelial Fibroma, Localized Fibrous Mesothelioma, Soft tissue solitary fibrous tumor, SFT, Hemangiopericytoma
Parent(s)
Fibroblastic Neoplasm
Children
Central Nervous System Solitary Fibrous Tumor/Hemangiopericytoma, Malignant Solitary Fibrous Tumor, Liver Solitary Fibrous Tumor, Pleural Solitary Fibrous Tumor, and Peritoneal Solitary Fibrous Tumor
OncoTree Name
Solitary Fibrous Tumor/Hemangiopericytoma
OncoTree Code
SFT

References

1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 8. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.