Overview

NCI Definition: A low grade childhood congenital malignant neoplasm arising from the kidney. It is characterized by the presence of fibroblastic cells. The majority of cases occur in the first year of life. Complete excision is usually associated with an excellent prognosis. [1]

Significant Genes in Congenital Mesoblastic Nephroma

ETV6 +

NTRK1 +

NTRK2 +

NTRK3 +

Disease Details

Synonyms
CMN, STROMAL NEPHROMA, MALIGNANT, Mesoblastic Nephroma
Parent(s)
Mesoblastic Nephroma
Children
Cellular Congenital Mesoblastic Nephroma and Classic Congenital Mesoblastic Nephroma

References

1. National Cancer Institute. NCI Thesaurus Version 18.11d. https://ncit.nci.nih.gov/ncitbrowser/ [2018-08-28]. [2018-09-21].

2. The AACR Project GENIE Consortium. AACR Project GENIE: powering precision medicine through an international consortium. Cancer Discovery. 2017;7(8):818-831. Dataset Version 6. This dataset does not represent the totality of the genetic landscape; see paper for more information.

3. All assertions and clinical trial landscape data are curated from primary sources. You can read more about the curation process here.